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Cerebral sphingolipidoses a symposium on Tay-Sachs' disease and allied disorders.
Başlık:
Cerebral sphingolipidoses a symposium on Tay-Sachs' disease and allied disorders.
Yazar:
Symposium on the Cerebral Sphingolipidoses (2nd : 1961 : Brooklyn and New York)
ISBN:
9781483196480
9781483221519
Toplantı Adı Girişi:
Yayın Bilgileri:
New York, Academic Press, 1962.
Fiziksel Tanımlama:
1 online resource (xvii, 456 pages) illustrations (some color)
Genel Not:
Sponsored by the Isaac Albert Research Institute of the Jewish Chronic Disease Hospital, the State University of New York, Downstate Medical Center, and the National Tay-Sachs Association.
İçerik:
Front Cover; Cerebral Sphingolipidoses: A Symposium on Tay-Sachs' Disease and Allied Disorders; Copyright Page; CONTRIBUTORS AND PARTICIPANTS; PREFACE; ACKNOWLEDGMENTS; Table of Contents; Chapter 1.Biopsy Diagnosis of Neurologic Diseases in Children, with Emphasis on the Lipidoses; Appendix; REFERENCES; Chapter 2.Pathogenesis of White Matter Changes in Tay-Sachs Disease; Source of Data and Methods; Clinical Observations; Gross Pathologic Features; Histologic Studies of Cerebral White Matter; Chemical Studies; Discussion; Summary; REFERENCES
Chapter 3.On the Pigment Variant of Amaurotic IdiocyHistological Observations; Histochemical Observations; Discussion; Summary; REFERENCES; Chapter 4. Electron Microscopy of the Cerebrum in Tay-Sachs' Disease; REFERENCES; Chapter 5.Comparative Histologic, Histochemical, and Electron Microscope Studies of Rectal Biopsies in a Case of Adult Hereditary Cerebromacular Degeneration; Case Report; Material and Methods; Histologic Findings; Histochemical Methods; Electron Microscope Studies; Discussion; Summary; REFERENCES; Chapter 6.The Cerebral Pathology of Infantile Gaucher's Disease; Introduction
Case ReportsPathological Findings; Comments on the Tissue Lipid Analyses; Discussion; Summary; REFERENCES; Chapter 7.Cerebral Lipidosis of Unclear Nature; Case Report; Histological Results; Chemical Observations; Comment; Summary; REFERENCES; Chapter 8.The Sphingolipids from the Spleen of a Case of Lipidosis; Methods; Results and Discussion; ACKNOWLEDGMENTS; REFERENCES; Chapter 9.Lipid Deposits in the Brain in Nonspecific Conditions Histochemically Like Those in the Lipidoses; Metachromatic Materials; Periodic Acid-Schiff Positive Materials; Cholesterol; Summary; REFERENCES
Chapter 10.Vacuolized Blood Lymphocytes in the Lipidoses and Other Central Nervous System Diseases with Special Reference to Histochemical Studies1Summary; REFERENCES; Chapter 11.Concepts of Dysmyelination; Introduction; The Primary Diseases of the Myelin Sheath; Questions on the Value of Histology in Studying Myelin; Relationship between the Leucodystrophies and the Lipidoses; Pathogenesis of the Leucodystrophies; Dysmyelination: A General Hypothesis; REFERENCES; Chapter 12. Alkali-Stable Choline Phospholipids (""Sphingomyelin"") in Tissue of Amaurotic Idiocies; Introduction
Material and MethodsResults; Discussion; REFERENCES; Chapter 13.Abnormalities in Lipid Metabolism in Two Members of a Family with Niemann-Pick Disease; Chemistry; REFERENCES; Chapter 14. The Chemical Pathology of Krabbe Disease and Metachromatic Leucodystrophy; ACKNOWLEDGMENTS; REFERENCES; Chapter 15.Determination of Alkali-Stable Phospholipids, Plasmalogens, and Phosphatidyl Compounds in Tissues by Phosphorus Analysis; Experimental; Discussion; Summary; REFERENCES; Chapter 16.Quantitative Fractionation of Complex Lipid Mixtures; Silicic Acid Column Chromatography
Özet:
Cerebral Sphingolipidoses: A Symposium on Tay-Sach's Disease and Allied Disorders is a collection of papers presented at the 1961 Symposium on the Cerebral Sphingolipidoses, held in Isaac Albert Research Institute of the Jewish Chronic Disease Hospital and the Downstate Medical Center of the State University of New York. The contributors demonstrate the significance attached to an intensive study of Tay-Sach's and allied diseases. A unique feature of the Symposium was the constant awareness of the clinical implications of the fundamental studies presented. This book is organized into three sec.
Başlık Ek Girişi:
Sphingolipidoses.
Elektronik Erişim:
ScienceDirect http://www.sciencedirect.com/science/book/9781483196480Mevcut:*
Yer Numarası | Demirbaş Numarası | Shelf Location | Lokasyon / Statüsü / İade Tarihi |
---|---|---|---|
RC632 .S67 S93 1961 | 1176801-1001 | Elsevier E-Kitap Koleksiyonu | Arıyor... |
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